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                                Health Topics 
                                
                                
                                    Healthy Living
                                
                                
                                
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            | April 2012 |  
            | Physiotherapy Managing Haemophilia |  
            | Dr Siju K Paul |  
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                        |  | Haemophilia is a genetic                 bleeding disorder                 characterized by the inability                 of blood to clot. It is due                 to the deficiency or absence of one                 of the clotting proteins called Factor                 VIII (Haemophilia A) or Factor IX               (Haemophilia B) in blood. |  
                        | It is in this context that the effort of countless midwives to help with the process of childbirth has to be appreciated, as the International Midwives’ Day falls on May 5th. It was only in the early 1900s with the increasing availability of hospitals that more women began going there for their delivery, as against planning births at home with little medication.
 
 The bleeding tendency in people with Haemophilia may vary according to the severity of gene defects. The bleeding will not be faster but more prolonged than in normal people. In mild and moderate cases of haemophilia, bleeding occurs after trauma or surgical procedures, but in severe form of Haemophilia bleeding happens spontaneously into joints and muscles. The clinical manifestations of internal bleeding include swelling, severe pain, warmth, restricted movements and inability to move the limbs. Whenever such bleeding occurs, haemophilia patients have to be infused with antihaemophilic factor concentrate to control or stop bleeding followed by intense physiotherapy to get back the normal functions of joints and muscles.
 
 In haemophiliacs, the repeated bleeding into the same joints or muscles will result in the evolvement of TARGET joints and muscles. The common target joints for bleeding are knees, elbows, ankles and the target muscles are psoas and calf muscles. The golden rule of physiotherapybased management in haemophilia is DEVELOPING GOOD MUSCLE STRENGTH and JOINT STABILITY. It is required to exercise regularly for a period of minimum three to six months to gain good muscle strength. Activities like cycling and swimming can also help to improve muscle strength
 
 Therapeutic Home Gym Kit: It consists of a pair of squeezable balls, sand bags with a zip, rubber bands having varying tensile strength.
 
 
 Ball ExercisesFor hand and shoulder muscles 
                            It will strengthen entire muscles of     the hand, forearm, arm and shoulder     girdleHold the soft balls.t Squeeze by tightening whole upper     limb muscles. 
 
 Sand Bag ExercisesPsoas muscle strengthening 
                            Quadriceps muscle strengtheningSit comfortably in a chair with back support.Keep the sand bag on your thigh.Lift the leg up by bending the hip.     It helps to prevent repeated hip     muscle bleeding by strengthening the     psoas muscles. 
                            It helps to improve knee joint stability and mobility by strengthening the quadriceps muscles.Sit comfortably in a chair with back support.Keep the sand bag on your ankle.Lift the leg by straightening the     knees.     It helps to improve knee joint stability     and mobility by strengthening the     quadriceps muscles. Rubber Band ExercisesTriceps strengthening 
                            Hamstring muscle strengtheningHold the rubber band.Stretch out the band by straightening     the elbow.It helps in preventing/correcting     the flexion deformity of elbow by     strengthening the triceps muscles 
 
                            Ankle dorsi flexors strengtheningSit comfortably in a chair with back support.Put the leg in rubber band loop which     is fixed at right angle to a heavy     object.Stretch the band by bending the     knee.     It helps to improve knee joint by     strengthening the hamstring muscles. 
                            Ankle plantar flexors strengtheningSit on the bed with legs straight.Put rubber band loop on the forefoot.     Stretch the band by raising the foot     up.     It helps to improve ankle joint stability     and mobility by strengthening the     anterior tibial and peroneal muscles. 
                            It helps to prevent calf muscle   bleed, and improves ankle joint by   strengthening the calf muscles.Sit on the bed with leg straight.Put rubber band loop on the foot.Hold the band steady with hand.Stretch the band by pushing the foot   down. 
 
 
                            
                                
                                    | How To Use The Kit? 
                                        Each exercise has to hold           for 10 seconds (a count of           10), followed by 5 secondsrelaxation before repeating.           t Each exercise starts with a           minimum weight. Gradually           progress by increasing the           weight and the number of           repetitions to achieve a target           weight and repetitions and           continue the same.
Exercise regularly with the               kit to develop and maintain               muscle strength that will avoid               / reduce repeated bleeding.Apply ice to exercising               muscles and joints for 10-15               minutes after completing the               exercises to avoid any chance               of repeated bleedings.Stop the exercise if bleeding               occurs in between and consult               the physiotherapist before               starting again |  |  
                
                    
                        | Dr Siju K Paul is Consultant Physiotherapist Haemophilia Society, Bangalore |  |  |